Chronicles of Young Scientists

SHORT COMMUNICATION
Year
: 2012  |  Volume : 3  |  Issue : 1  |  Page : 86--88

Desmoplastic small-round-cell tumor presenting as a Sister Joseph nodule


Arcot Rekha1, Shalinee Rao1, J Thanka2, S Rajendiran2, A Ravi1 
1 Department of Surgery, Sri Ramachandra Medical College and Research Institute, Chennai, Tamil Nadu, India
2 Department of Pathology, Sri Ramachandra Medical College and Research Institute, Chennai, Tamil Nadu, India

Correspondence Address:
Arcot Rekha
30, 3rd Main Road, Subashree Nagar Extension, Mugallivakkam, Porur, Chennai - 600 116, Tamil Nadu
India

We document a rare presentation of desmoplastic small-round-cell tumor (DSRCT) in a 25-year-old male. He presented with a nodular swelling in the umbilical region that was clinically suggestive of Sister Joseph nodule. Imaging studies showed multiple nodules over the peritoneum and the gastrointestinal endoscopies showed no lesions. An excision biopsy of the umbilical lesion showed small round cells with dense desmoplasia and immunohistotyping confirmed the diagnosis of DSRCT. Desmoplastic small-round-cell tumor is notable for its poor prognosis.


How to cite this article:
Rekha A, Rao S, Thanka J, Rajendiran S, Ravi A. Desmoplastic small-round-cell tumor presenting as a Sister Joseph nodule.Chron Young Sci 2012;3:86-88


How to cite this URL:
Rekha A, Rao S, Thanka J, Rajendiran S, Ravi A. Desmoplastic small-round-cell tumor presenting as a Sister Joseph nodule. Chron Young Sci [serial online] 2012 [cited 2019 Sep 17 ];3:86-88
Available from: http://www.cysonline.org/article.asp?issn=2229-5186;year=2012;volume=3;issue=1;spage=86;epage=88;aulast=Rekha;type=0